Female Genital Development Richard Schlussel M.D. Assistant

Female Genital Development Richard Schlussel M.D. Assistant Professor Department of Urology Columbia University

Normal development Duplication Agenesis UG Sinus Imperforate hymen CAH

Hypospadias

Hypospadias repair

Hypospadias repair

Paramesonephric duct – A.K.A. Mullerian Duct – Becomes future Fallopian tubes Uterus Upper 2/3 vagina

VAGINAL AND UTERINE DUPLICATION

Bicornuate Uterus

Didelphys uterus

Unicornuate Uterus

Symptom – Blood persists despite tampon during menses Complete Vaginal Duplication

Symptom – Upper vagina fills with blood during menses

1 in 5,000 births Mayer-Rokitansky-KüsterHauser Syndrome

VAGINAL AGENSIS

Normal Hymenal Ring

Imperforate hymen Mucous due to maternal hormones

Intra-op drainage of imperf hymen

UROGENITAL SINUS

UROGENITAL SINUS

X X CONGENITAL ADRENAL HYPERPLASIA (CAH)

CAH 46 XX

Association with Urinary Tract Anomalies – Renal agenesis – Ectopic ureters